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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Actin
Muscle fibrosis
Bioinformatics
Muscle stem cells
C2C12 cells
MUTATIONS
Botulinum neurotoxin
Human
OPMD
DNA methylation
Andermann syndrome
APOPTOSIS
Muscle strength
Nuclear envelope
Myopathies
Transcriptomics
Geriatric assessment
Regeneration
Pax7
Sarcopenia
Anti-fibrotic pharmacotherapies
CD49d
Myosin
Thérapie génique
C2 domains
FAPs
2-D PAGE
Neuromuscular junction NMJ
Muscle dystrophy
Alphavirus
Biopsies humaines
Haploinsufficiency
Atrophy
Myopathy
Intercellular communication
AAV
Myoblast
CS
Aav-U7
DMD
Metabolism
Pharyngeal muscle
Annexin A2
Antisens oligonucleotides
Fibrosis
Aged
AAV vectors
Xenograft
Myositis
AChR antibodies
CNOT6L
Biomarker
Ageing
Bile salt hydrolases
PABPN1 agregates
Dystrophin
Autoimmune diseases
Differentiation
Muscle
Akt
ARN
Satellite cells
Myogenesis
Autologous
Gene therapy
Oculopharyngeal muscular dystrophy
Skeletal muscle
Accelerometry
Satellite cell
Exon-skipping
Bioinformatique
DUX4
Adipose tissue
Calcium
Myotube
Agrégats de PABPN1
AUTOPHAGY
PABPN1
Dysferlin
Dysferlinopathy
BINDING SPECIFICITY
Duchenne muscular dystrophy
ALS
Lamins
Functional genomics
Antiserum
Gene replacement
Triplet expansion disease
GENE
FSHD
Inflammation
Arbovirus
Cell therapy
Cross-bridge kinetics
RNA
Aggregate
Anti-acetylcholine receptor antibodies
Myoblasts
Dystrophie musculaire oculopharyngée
Alzheimer's disease